Abstract :Portal annular pancreas is a uncommon congenital anomaly resulting from fusion of the pancreatic parenchyma around the portal vein. Its causing portal cavernoma formation and association with dorsal pancreatic agenesis is rare
Case report We report a 51-year-old female who underwent contrast enhanced computed tomography for vague right hypochndrial pain. On CECT abdomen images there was presence of rind of pancreatic tissue around the portal vein cause in its luminal narrowing with proximal dilation of portal vein tributaries with cavernoma formation. There was also presence of agenesis of dorsal pancreas in this patient. Conclusion This variant of portal annular pancreas with cavernoma formation associated with dorsal pancreatic agenesis has not yet been reported and we propose a new CT classification of the same.